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Revista Portuguesa de Estomatologia,
Medicina Dentária e Cirurgia Maxilofacial

rev port estomatol med dent cir maxilofac. 2018;59(4):221-224

Case report

Peters-plus syndrome: oral health approach

Maíra Roberta Lima Viga, Emílio Carlos Sponchiado Júnior*, Pollyanna Oliveira Medina,
Ary de Oliveira Alves Filho, Simone Assayag Hanan

Dental School, Federal University of Amazonas, Manaus, AM, Brazil

a r t i c l e i n f o a b s t r a c t

Article history: The aim of this paper is to report a clinical case of a male patient with Peters-plus syndrome.
Received 3 September 2018 This syndrome is a rare, autosomal recessive congenital disorder. It is diagnosed by the
Accepted 19 January 2019 presence of ocular changes associated with delayed psychomotor development, cardiac
Available online 6 February 2019 defects, and characteristic facial features, such as cleft lip, hypertelorism, narrow eyes, prom-
inent forehead, and hearing loss. Clinical examination revealed gingival hyperplasia in the
Keywords: upper and lower arches resulting from the use of phenobarbital, associated with the presence
Cleft lip-palate of a large amount of dental biofilm, and active white spot lesions in the upper deciduous
Dental care incisors. Replacement of the anticonvulsant medication was requested. Guidelines on oral
Dentistry and dietary hygiene habits as well as topical application of fluoride varnish were provided.
Gingival hyperplasia Hyperplasia was reversed in 2 weeks and the patient has been receiving follow-up care. The
Peters anomaly patient is being monitored and his oral condition has improved. (Rev Port Estomatol Med
Dent Cir Maxilofac. 2018;59(4):221-224)
© 2018 Sociedade Portuguesa de Estomatologia e Medicina Dentária.
Published by SPEMD. This is an open access article under the CC BY-NC-ND license
(http://creativecommons.org/licenses/by-nc-nd/4.0/).

Síndrome de Peters-plus: abordagem odontológica

r e s u m o

Palavras-chave: O objetivo deste artigo é relatar um caso clínico de um paciente do sexo masculino com
Fenda palatina a síndrome de Peters-plus. Esta síndrome é uma doença congénita rara, autossómica re-
Atendimento odontológico cessiva, diagnosticada pela presença de alterações oculares associadas ao atraso no de-
Medicina dentária senvolvimento psicomotor, defeitos cardíacos e características faciais próprias, como lábio
Hiperplasia gengival leporino, hipertelorismo, olhos estreitos, fronte proeminente e perda auditiva. O exame
Síndrome de Peters clínico revelou hiperplasia gengival nos arcos superior e inferior decorrentes do uso de
fenobarbital, associada à presença de grande quantidade de biofilme dentário e lesões
brancas ativas nos incisivos decíduos superiores. Foi solicitada a substituição da medica-

* Corresponding author.
E-mail address: spemilio@ufam.edu.br (Emílio Carlos Sponchiado Júnior).
http://doi.org/10.24873/j.rpemd.2018.11.422
1646-2890/© 2017 Sociedade Portuguesa de Estomatologia e Medicina Dentária. Published by SPEMD.
This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).